Conclusion: Histochemical MGT staining light shows RRF, accumulation of abnormal mitochondrials , especially the paracrystaline inclusion which plays an important role in diagnosis.

结论：MGT染色发现破碎红纤维，电镜下线粒体堆积、形态异常，特别是线粒体内晶状包涵体，对本病的诊断有重要价值。